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PO:37:270 | Efficacy of iloprost as a therapy for skin ulcers in cryofibrinogenemia and cryoglobulinemia: a complex case in a fragile patient Luca Keller Sarmiento1, Amelia Spinella2, Marco De Pinto2, Giorgia Roveta1, Dilia Giuggioli1|2. | 1Università degli Studi di Modena e Reggio Emilia, Modena, Italy; 2Unità di Reumatologia del Policlinico di Modena, Modena, Italy.
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PO:35:221 | Cryofibrinogen: a cold case. Characteristics and clinical outcomes from a cryofibrinogen positive cohort Daniele Catameró1, Andrea Cito1, Cristiana Colaprico1, Teresa Caferri1, Teresa Troiano1, Anna Marinaccio1, Marco Fornaro1, Giuseppe Lopalco1, Florenzo Iannone1. | 1Unit of Rheumatology , Department of Precision and Regenerative Medicine, Area Jonica DiMePRe-J, University of Bari, Bari, Italy.
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PO:32:181 | Digital ulcers predict enhanced Peak Systolic Velocities at internal and external Carotid in Systemic Sclerosis Patients Eugenio Capparelli1, Francesco Lapia2, Luca Clerici2, Eleonora Zaccara1, Giusy Cinzia Moltisanti2, Francesca Capelli2, Daniela Bompane1, Paola Faggioli1, Antonino Mazzone2 | 1UOC Reumatologia, ASST Ovest Milanese, Legnano, Milano, Italy; 2UOC Medicina Interna, ASST Ovest Milanese, Legnano, Milano, Italy
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PO:32:183 | Innovative use of integra dermal regeneration template on systemic sclerosis digital ulcers: a case report Elena Vanni1, Martina Orlandi1|2, Amelia Spinella2, Valentina Pinto3, Massimo Pinelli3, Dilia Giuggioli1|2 | 1Reumatologia, Università di Modena e Reggio Emilia; 2Reumatologia, Azienda Ospedaliero-Universitaria Policlinico di Modena; 3Chirurgia Plastica, Università di Modena e Reggio Emilia e Azienda Ospedaliero-Universitaria, Policlinico di Modena, Italy
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PO:30:160 | A rare case of juvenile systemic sclerosis Marta Arese1|2, Francesco Baldo3, Stefania Costi3, Achille Marino3, Cecilia Chighizola1|3, Roberto Felice Caporali1|2 | 1Azienda Ospedaliera Universitaria Senese, Università degli Studi di Siena; 2Reumatologia Clinica, ASST Gaetano Pini-CTO, Milano, Italy
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PO:31:165 | Prevalence and incidence of skin telangectasia and their association with clinical features: analysis of the European Scleroderma Trials and Research cohort Gemma Lepri1, Lorenzo Tofani2, Silvia Bellando Randone1, Veronica Batani3, Paolo Airò4, Patricia Carreira5, Joerg Henes6, Alexandra Balbir Gurman7, Florenzo Iannone8, Antonella Marcoccia9, Luc Mouthon10, Branimir Anic11, Carolina De Souza Müller12, Armine Haroyan13, Ana Cristina Cordeiro14, Serena Guiducci And Eustar Coll1. | 1University of Florence, Dept of Experimental and Clinical Medicine, AOU Careggi, Division of Rheumatology Florence Italy; 2University of Florence, Dept of Statistics, Informatics, Applications, Florence, Italy; 3Unit of Immunology, Rheumatology, Allergy and Rare Diseases UnIRAR, IRCCS San Raffaele, Milano, Italy; 4Scleroderma Unit, UOC Rheumatology and Clinical Immunology, ASST Spedali Civili, Brescia, Italy; 5Dept of Rheumatology, 12 de Octubre University Hospital, Madrid, Spain; 6Centre for Interdisciplinary Rheumatology, Immunology and autoimmune diseases INDIRA, University Hospital Tuebingen, Tuebingen, Germany; 7Rheumatology Institute, Rambam Health Care Campus Haifa Israel; 8Dept of Precision and Regenerative Medicine and Ionian Area, University of Bari, Bari, Italy; 9Interdisciplinary Reference Center for Systemic Sclerosis CRIIS Sandro Pertini Hospital, Rome, Italy; 10Dept of Internal Medicine, Cochin Hospital, Paris Cité University, Paris, France; 11Div Clinical Immunology and Rheumatology, Dept Internal Medicine, School of Medicine, University Hospital Center Zagreb, Zagreb, Croatia; 12Rheumatology Division, Hospital de Clínicas da Universidade Federal do Parana, Curitiba, Brazil; 13Dept of Rheumatology, Yerevan State Medical University of Armenia, Yerevan, Armenia; 14Servico Reumatologia Hospital Garcia de Orta Almada, Almada, Portugal.
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PO:33:199 | Prevalence and clinical associations of antiphospholipid antibodies in patients with systemic sclerosis in the SPRING-SIR registry Antonio Tonutti1|2, Ilaria Cavazzana3, Angela Ceribelli1|2, Maria De Santis1|2, Giacomo De Luca4|5, Maria Grazia Lazzaroni3, Franco Franceschini3, Carlo Selmi1|2, Valeria Riccieri6, Silvia Laura Bosello7, Fabio Cacciapaglia8, Veronica Codullo9, Francesca Ingegnoli10, Dilia Giuggioli11, Rossella De Angelis12, Clodoveo Ferri11, Marco Matucci-Cerinic4|5 | 1Department of Biomedical Sciences, Humanitas Universityce Pieve Emanuele, Milan, Italy; 2Rheumatology and Clinical Immunology, IRCCS Humanitas Research Hospital Rozzano, Milan, Italy; 3Rheumatology and Clinical Immunology - ASST Spedali Civili Brescia - Department of Clinical and Experimental Sciences - Brescia, Italy; 4Vita-Salute San Raffaele University Milan, Italy; 5Unit of Immunology, Rheumatology, Allergy and Rare Diseases UnIRAR and INFLAGE Initiative, IRCCS San Raffaele Hospital Milan, Italy; 6University of Rome La Sapienza Rome, Italy; 7Catholic University of Sacred Heart Rome, Italy; 8LUM University Bari, Italy; 9Rheumatology Unit, Fondazione IRCCS Policlinico San Matteo Pavia, Italy; 10University of Milan Milan, Italy; 11University of Modena and Reggio Emilia Modena, Italy; 12Politechnic University of Marche Ancona, Italy
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PO:36:245 | Uncovering clinical and demographic differences in major organ involvement versus benign Behçet’s disease: insights from a single-centre study Federica Di Cianni1, Antonello Sulis1, Maria Laura Manca2, Rosaria Talarico1, Marta Mosca1. | 1Rheumatology Unit, University of Pisa, Pisa, Italy; 2Department of Clinical and Experimental Medicine and Department of Mathematics, University of Pisa, Pisa, Italy.
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PO:24:068 | Case Report: ‘Spontaneous Pneumomediastinum in a Patient with MDA5-Positive Dermatomyositis and Severe Pulmonary Fibrosis’ Carlotta Braga1, Margherita Rizzo1, Marta Raschellà1, Beatrice Maranini1, Gioacchino Schifino2, Aldo Carnevale3, Marcello Govoni1, Andrea Lo Monaco1 | 1Rheumatology Unit, Department of Medical Sciences, University of Ferrara and Azienda Ospedaliero-Universitaria S. Anna Ferrara, Italy; 2Respiratory Medicine Unit, Department of Cardio-Thoracic-Vascular Pathologies, Arcispedale Sant'Anna, Ferrara, Italy; 3Radiology Unit, Department of Translational Medicine, University of Ferrara, Italy
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CO:06:1 | Predictors of damage accrual in a monocentric cohort of patients with Behçet’s syndrome (BS) evaluated with BS overall damage index in real-life clinical practice Giulia Voltarel1|2, Francesca Crisafulli1|2, Alba Chiara Pozzi1|2, Anita Melzani2, Micol Frassi1, Ilaria Cavazzana1|2, Franco Franceschini1|2, Paolo Airò1. | 1Rheumatology and Clinical Immunology Unit - ERN ReCONNET, ASST Spedali Civili of Brescia; 2Department of Clinical and Experimental Sciences, University of Brescia, Italy
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PO:32:184 | Assessing the burden of Sars-Cov2 in systemic sclerosis-related interstitial lung disease patients: functional, clinical and therapeutic outcomes from an Italian cohort, a retrospective study Andrea Cito1, Greta Giulia Dipietrangelo1, Daniele V. A. Sabella1, Marco Fornaro1, Fabio Cacciapaglia1, Giuseppe Lopalco1, Florenzo Iannone1. | 1AOUC Policlinico di Bari - Reumatologia Universitaria, Bari, Italy.
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PO:33:195 | Evaluation of prevalence and role of anti-endothelin type a-receptor and anti-angiotensin ii type 1-receptor antibodies in a cohort of systemic sclerosis patients Clara Minerba1, Sara Ferrigno1, Antonella Grimaldi2, Noemi Aprile3, Daniela Costanza2, Laura Quarta2, Maria Rita Ricciardi2, Daniela Stasi3, Paola Conigliaro1, Alberto Bergamini1, Eugenio Quarta2, Maria Sole Chimenti1. | 1U.O.C. Reumatologia, Dipartimento di Medicina dei Sistemi, Università di, Roma, Tor Vergata, Roma, Italy; 2U.O.S.D. Reumatologia, P.O. Vito Fazzi Lecce Italy; 3U.O.C. Patologia clinica e Microbiologia, P.O. Vito Fazzi Lecce Italy.
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PO:17:253 | Unveiling the gap: a multicenter study on factors driving patient-physician discrepancies in assessing disease activity in systemic lupus erythematosus Giorgia Ingrid Gozzoli1, Micaela Fredi1, Federica Bonaso1, Silvia Ebe Lucia Della Pina1, Claudia Barison1, Irene Lorenzini4, Raffaele Pericotti4, Anna Mattiuzzo4, Marcelo Neto2, Sofia Azevedo3, Cláudia Oliveira3, Cesare Tomasi4, Luís Sousa Inês2, Franco Franceschini1. | 1Rheumatology and Clinical Immunology Unit, ASST Spedali Civili of Brescia, Brescia, Italy; 2Rheumatology Department, Centro Hospitalar Universitário de Coimbra - ULS Coimbra, Coimbra, Portugal; 3Rheumatology Department, ULS Aveiro, Aveiro, Portugal; 4Department of Clinical and Experimental Sciences, University of Brescia, Brescia, Italy.
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PO:30:155 | The role of nailfold videocapillaroscopy in the assessment of juvenile connective tissue diseases Marco Binda1, Beatrice Moccaldi1, Francesca Tirelli2, Anna Cuberli1, Andrea Benini1, Meneghel Alessandra2, Andrea Doria1, Francesco Zulian2, Elisabetta Zanatta1 | 1U.O.C. Reumatologia, Dipartimento di Medicina DIMED, Università degli Studi di Padova Padova, Italy; 2U.O.S.D. Reumatologia Pediatrica, Dipartimento per la Salute della Donna e del Bambino, Azienda Ospedaliera di Padova, Italy
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PO:33:197 | Systemic sclerosis and endothelial dysfunction: the passive leg movement technique in the assessment of no-mediated vascular impairment Silvia Guella1, Giovanni Baldassarre3, Alessandro Gratton2|3, Lucrezia Zuccarelli3, Elena Treppo2, Emma Di Poi2, Bruno Grassi3, Luca Quartuccio2|3 | 1SS Reumatologia-CMID Ospedale San Giovanni Bosco, Torino; 2Clinica di Reumatologia Ospedale Santa Maria della Misericordia, ASUFC, Udine; 3Dipartimento di Medicina, Università di Udine, Italy
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PO:31:172 | Age and timing of onset of Raynaud's phenomenon and first non-Raynaud sign/symptom as prognostic factors in systemic sclerosis: a retrospective analysis from the systemic sclerosis progression investigation registry of the Italian Society for Rheumatology Silvia Peretti1, Cosimo Bruni2, Silvia Laura Bosello3, Fabio Cacciapaglia4-5, Corrado Campochiaro6-7, Veronica Codullo8, Lorenzo Dagna6-7, Rossella De Angelis9, Giacomo De Luca6-7, Dilia Giuggioli10, Serena Guiducci1, Florenzo Iannone4, Francesca Ingegnoli11, Valeria Riccieri12, Marco Matucci Cerinic6-7, Clodoveo Ferri10-13, Silvia Bellando Randone1. | 1Division of Rheumatology, Scleroderma Unit, Department of Experimental and Clinical Medicine, University of Florence, AO, Firenze, Italy; 2Division of Rheumatology, University Hospital Zurich, University of Zurich, Zurich, Switzerland; 3Rheumatology Division, Catholic University of the Sacred Heart, Fondazione Policlinico Universitario A. Gemelli- IRCCS, Roma, Italy; 4Rheumatology Unit, Department of Precision and Regenerative Medicine-Ionian Area, University of Bari Aldo Moro, Bari, Italy; 5Reumatology Service, Internal Medicine Unit F.Miulli General Hospital, Acquaviva delle Fonti -Department of Medicine a, Bari, Italy; 6Unit of Immunology, Rheumatology, Allergy and Rare Diseases UnIRAR, Inflammation, Fibrosis and Ageing initiative INFL, Milano, Italy; 7Vita-Salute San Raffaele University, Milano, Italy; 8Department of Internal Medicine and Therapeutics, Università di Pavia, Italy; Division of Rheumatology, Fondazione IRCCS, Pavia, Italy; 9Rheumatology Unit, Department of Clinical and Molecular Sciences, Polytechnic University of Marche, Ancona, Italy; 10Rheumatology Unit, School of Medicine, University of Modena and Reggio Emilia, Modena, Italy; 11Division of Clinical Rheumatology, ASST Pini, Dept. of Clinical Sciences and Community Health, Research Center for Adul, Milano, Italy; 12Department of Rheumatology, Sapienza University of Rome, Roma, Italy; 13Rheumatology Clinic Madonna dello Scoglio Crotonei, Crotone, Italy.
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PO:36:253 | Lifestyle and Behçet's syndrome: a preliminary study on gender differences Pietro Leccese1, Angela Anna Padula1, Nancy Lascaro1, Salvatore D'Angelo1, Maria Carmela Padula1 | 1UOC Reumatologia AOR San Carlo, Potenza, Italy
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PO:31:169 | From Crisis to Chronicity: A Real-World Study of Renal Dysfunction in Systemic Sclerosis Stefano Stano1, Fabio Cacciapaglia1|2, Giorgia Campanale1, Simone Perniola1, Maria Morrone1, Andrea Cito1, Vincenzo Venerito1, Maria Grazia Anelli1, Giuseppe Lopalco1, Florenzo Iannone1 | 1Rheumatology Unit - Department of Precision and Regenerative Medicine, Jonian Area DiPReMeJ, University of Bari Bari, Italy; 2Rheumatology Service, Internal Medicine Unit F. Miulli General Hospital, Department of Medicine and Surgery, LUM Casamassima, Italy
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PO:23:055 | Overlap of systemic sclerosis and Sjögren’s disease: insights from an Italian case-control study Stefano Stano1, Fabio Cacciapaglia1|2, Maria Morrone1, Simone Perniola1, Marco Capodiferro1, Marco Fornaro1, Laura Coladonato1, Giuseppe Lopalco1, Florenzo Iannone1. | 1Rheumatology Unit - Department of Precision and Regenerative Medicine, Jonian Area DiPReMeJ, University of Bari, Bari, Italy; 2Rheumatology Service, Internal Medicine Unit F. Miulli General Hospital, Department of Medicine and Surgery, LUM Casamassima Italy.
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