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CO:11:5 | Laboratory preliminary results from an open label, prospective, phase ii descriptive pilot trial of belimumab therapy for refractory and/or non criteria manifestations of antiphospholipid syndrome Alice Barinotti1, Massimo Radin1, Irene Cecchi1, Beatrice Ala1, Chiara Raymondi1, Elena Rubini1, Silvia G. Foddai1, Lois Ira Maniulit Capulong1, Alessio Conti1, Alessandro Morotti1, Dario Roccatello1, Roberta Fenoglio1, Savino Sciascia1. | 1Università di Torino, Italy.
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PO:35:220 | IgG anti-pentraxin 3 autoantibodies distinguish eosinophilic granulomatosis with polyangiitis from severe eosinophilic asthma and chronic rhinosinusitis with nasal polyps Eleonora Fiorin1, Anna Ghirardello1, Federica Davanzo1, Luca Iorio1, Marta Codirenzi1, Roberta Prevedello1, Roberto Padoan1, Andrea Doria1. | 1Università di Padova, Dipartimento di Medicina DIMED, UOC di Reumatologia, Padova, Italy.
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PO:10:157 | Sjögren’s syndrome with cryoglobulinemia associated with POEMS syndrome Andrea Mazzon1, Elena Bianchi1, Virginia Berlengiero1, Luca Cantarini1, Bruno Frediani1, Enrico Selvi1 | 1Azienda Ospedaliera Universitaria Senese Le Scotte, Siena, Italy
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PO:03:035 | Biomarkers of Gut Epithelial Damage, Microbial Translocation, and Innate Immune Activation Characterize Patients with Axial Psoriatic Arthritis from Psoriasis Patients: Soluble Biomarker Analysis Insights from the ATTRACT Study Giulia Marchionni1, Valentino Paci1, Silvia Svegliati1, Raffaella Sordillo1, Federico Fiorini1, Melania Giannoni1, Anna Campanati1, Raissa Di Zio1, Devis Benfaremo1, Giuseppe Lopalco2, Florenzo Iannone2, Ennio Lubrano3, Alberto Cauli4, Gianluca Moroncini1, Dennis Poddubnyy5, Fabian Proft6, Michele M Luchetti Gentiloni1 | 1Marche Polytechnic University and Azienda Ospedaliero-Universitaria delle Marche, Ancona, Italy; 2University of Bari, Bari, Italy; 3Molise University, Campobasso, Italy; 4University of Cagliari, Azienda Ospedaliero Universitaria di Cagliari, Monserrato, Italy; 5University of Toronto, Toronto, Canada; 6Charité-Universitätsmedizin, Berlino, Germany
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PO:22:033 | Unraveling VEXAS syndrome: when skin manifestations and monoclonal gammopathy precede hematological myeloid alterations Laura Di Centa1, Simone Longhino1, Valeria Manfrè1, Stefania Sacco1, Luca Quartuccio1 | 1ASST Papa Giovanni XXIII, Bergamo, Italy
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PO:14:205 | Primary antiphospholipid antibody syndrome: association between new classification criteria manifestations and a higher-risk disease phenotype Sara Ferrigno1, Vittorio Forte2, Marco Panetta1, Sergio Lisena1, Giorgia Ranucci2, Luigi De Marco1, Elisabetta Greco1, Alberto Bergamini1, Maria Sole Chimenti1, Paola Conigliaro1. | 1Rheumatology, allergology and clinical immunology, Department of Systems Medicine, University of Rome Tor Vergata, Rome, Italy; 2Hematology, Department of Biomedicine and Prevention, University of Rome Tor Vergata, Rome, Italy.
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PO:10:144 | Management of pure red cell aplasia as the onset of systemic lupus erythematosus: a case report Chrystel Carolin Navarrete Cadena1, Marika Tardella1 | 1Università Politecnica delle Marche Jesi, Ancona, Italy
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PO:28:116 | Glandular involvement in autoimmune diseases: a spectrum of differential diagnosis Francesca Petrillo1, Caterina Ricordi1, Caterina Tomassini1, Luca Cimino3, Giorgia Citriniti2, Fabio Brandolino2, Chiara Marvisi1, Carlo Salvarani1 | 1S.C. Reumatologia; 2S.C. Reumatologia; 3S.S.D. Immunologia Oculare, Università di Modena e Reggio Emilia, Arcispedale Santa Maria Nuova, Reggio Emilia, Italy
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Real-life effectiveness of rituximab in different subsets of idiopathic inflammatory myopathies
2275PDF: 459SUPPLEMENTARY MATERIAL: 345 -
PO:37:270 | Efficacy of iloprost as a therapy for skin ulcers in cryofibrinogenemia and cryoglobulinemia: a complex case in a fragile patient Luca Keller Sarmiento1, Amelia Spinella2, Marco De Pinto2, Giorgia Roveta1, Dilia Giuggioli1|2. | 1Università degli Studi di Modena e Reggio Emilia, Modena, Italy; 2Unità di Reumatologia del Policlinico di Modena, Modena, Italy.
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PO:22:039 | A rare form of interstitial lung disease: granulomatous and lymphocytic interstitial lung disease Francesca Cozzini1|2, Francesco Falco1, Alberto Cavazza1, Lucia Spaggiari3, Chiara Marvisi1, Francesca Petrillo1|2, Caterina Ricordi1|2, Francesco Muratore1|2, Fabio Brandolino1, Ilaria Chiapparoli1, Carlo Salvarani1|2, Andreina Manfredi1|2 | 1IRCCS Policlinico San Matteo, UO di Reumatologia, Pavia; 2Università degli studi di Modena e Reggio Emilia, Modena, Italy
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CO:11:2 | Systemic lupus erythematosus with major neuropsychiatric involvement treated with anifrolumab: literature review and a case report Giulia Rizzo1, Fabio Congiu1, Elisabetta Chessa2, Marta Paola Pireddu1, Elena Ragusa1, Alessandra Oliva1, Marianna Salis1, Alberto Cauli1|2, Matteo Piga1|2 | 1SC Reumatologia, Dipartimento di Scienze Mediche e Salute Pubblica, Università di Cagliari Italy; 2SC Reumatologia, AOU Cagliari Italy
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PO:26:087 | Rituximab versus glucocorticoids for IgG4-related disease: a European retrospective multi-center study of 167 patients Marco Lanzillotta1, Jens Vikse2, Elisabetta Goni3, Jasmin Mahajne1, Veronica Batani1, Lorenzo Dagna1, Emanuel Della-Torre1 | 1Unit of Immunology, Rheumatology, Allergy, and Rare Disease, IRCCS Ospedale san Raffaele Milano, Italy; 2Department of Rheumatology, Stavanger University Hospital, Stavanger, Norway; 3Department of Medicine II, University Hospital, Ludwig Maximilian University Munich, Munich Germany
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PO:11:172 | Not all vasculitis look the same: a difficult diagnosis Marta Arese1|2, Miriam Perino1|2, Sofia Aliprandi1|2, Antonella Murgo2, Maria Gerosa1|2, Roberto Felice Caporali1|2 | 1UOC Reumatologia AOR San Carlo, Potenza; 2Reumatologia Clinica, ASST Gaetano Pini-CTO, Milano, Italy
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PO:19:286 | Genetic testing reveals an unexpected case of mevalonate kinase deficiency in a 37-year-old patient with AA renal amyloidosis and good response to colchicine Francesca Crisafulli1, Paolo Airò2, Federica Mescia3, Gianmarco Lugli3, Gianfranco Savoldi4, Claudia Izzi3|5, Federico Alberici3, Marco Cattalini6, Franco Franceschini1, Micol Frassi2. | 1Rheumatology and Clinical Immunology Unit, ASST Spedali Civili and University of Brescia, Brescia, Italy; 2Rheumatology and Clinical Immunology Unit, ASST Spedali Civili of Brescia, Brescia, Italy; 3U.O Nefrologia, ASST Spedali Civili di Brescia e Università degli Studi di Brescia, Brescia, Italy; 4Medical genetics Laboratory, Laboratory Department ASST Spedali Civili di Brescia, Brescia, Italy; 5Struttura Complessa di Genetica Clinica, ASST Spedali Civili di Brescia, Brescia, Italy; 6Pediatrics Clinic, University of Brescia and ASST Spedali Civili of Brescia, Brescia, Italy.
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S02:6 | Monocyte-Driven Inflammation and Inflammasome Activation in ANCA-Positive EGPA: Evidence of Persistent Immune Activation During Remission Chiara Baggio1, Luca Iorio1, Carlotta Boscaro2|3, Federica Davanzo1, Marta Tonello1, Mattia Albiero4, Andrea Doria1, Paolo Sfriso1, Roberto Padoan1, Francesca Oliviero1 | 1Rheumatology Unit, Department of Medicine, University of Padova, Italy; 2Department of Medicine, University of Padova, Italy; 3Veneto Institute of Molecular Medicine, Laboratory of Experimental Diabetology, Italy; 4Department of Surgery, Oncology, and Gastroenterology, University of Padova, Italy
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PO:16:241 | Prevalence and associated factors of premature ovarian insufficiency in women with systemic lupus erythematosus: the role of human herpesviruses HHV-7 and HHV-8 Margherita Rizzo1, Francesca Ruffilli1, Silvia Beltrami2, Daria Bortolotti2, Roberta Rizzo2, Carlo Garaffoni1, Ettore Silvagni1, Marcello Govoni1, Alessandra Bortoluzzi1 | 1UOC Reumatologia, Dipartimento di Scienze Mediche, Università di Ferrara e Azienda Ospedaliero-Universitaria S. Anna, Ferrara; 2Dipartimento di Scienze Chimiche, Farmaceutiche e Agrarie, Ferrara Italy
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