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PO:15:222 | Post-hoc analysis of the BeRLiSS-JS registry: efficacy of belimumab on thrombocytopenia Greta Hulej1, Margherita Zen1, Marisol Bracalenti1, Francesca Bottazzi2, Rossella De Angelis3, Giacomo Emmi4, Roberto Gerli5, Marcello Govoni6, Renato Lo Gullo7, Simone Negrini8, Luca Quartuccio9, Maurizio Rossini10, Carlo Salvarani11, Paola Tomietto4, Angelo Vacca12, Andrea Doria1, Luca Iaccarino1. | 1Università degli Studi di Padova, Padova, Italy; 2Università degli Studi di Pavia, Pavia, Italy; 3Università Politecnica delle Marche, Ancona, Italy; 4Università degli Studi di Trieste, Trieste, Italy; 5Università degli Studi Perugia, Perugia, Italy; 6Università degli Studi di Ferrara, Ferrara, Italy; 7Università degli Studi di Catania, Catania, Italy; 8Università degli Studi di Torino, Torino, Italy; 9Università degli Studi di Udine, Udine, Italy; 10Università degli Studi di Verona, Verona, Italy; 11Università degli Studi di Modena e Reggio Emilia, Modena, Italy; 12Università degli Studi di Bari .
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PO:14:202 | Use of anifrolumab in the treatment of the hematological manifestations of systemic lupus erythematosus: a single-centre case series Gaia Ferracane1|2, Jessika Dichiara1|2, Elena Manna1|2, Lorenzo Mattia Bianchessi1|2, Giovanni Zanframundo1|2, Serena Bugatti1|2, Veronica Codullo1|2, Lorenzo Cavagna1|2, Francesca Bottazzi1|2 | 1Department of Internal Medicine and Therapeutics, Università di Pavia; 2Division of Rheumatology, IRCCS Policlinico San Matteo, Pavia, Italy
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CO:06:3 | Clinical and laboratory markers for distinguishing VEXAS from Schnitzler's syndrome in male patients with skin involvement: insights from the International AIDA Network Registries Valeria Caggiano1, Jessica Sbalchiero1, Micol Frassi2, Andrea Hinojosa-Azaola3, Francesca Crisafulli2, Franco Franceschini2, Paolo Sfriso4, Sara Bindoli4, José Hernández-Rodríguez5, Henrique A. Mayrink Giardini6, Giuseppe Lopalco7, Florenzo Iannone7, Ombretta Viapiana8, Amato De Paulis9, Lorenzo Dagna10, Antonio Gidaro11, Serena Bugatti12, Matteo Piga13, Fabrizio Conti14, Rosetta Vitetta15, Cecilia Chighizola16, Marcello Govoni17, Giacomo Emmi18, Paola Triggianese19, Carmelo Gurnari19, Bruno Frediani1, Claudia Fabiani1, Luca Cantarini1, Antonio Vitale1, for the AIDA Network1 | 1Department of Medical Sciences, Surgery and Neurosciences, University of Siena; 2University of Brescia, Italy; 3Department of Immunology and Rheumatology, Mexico City, Mexico; 4Rheumatology Unit, University of Padova, Italy; 5Clinical Unit of Autoinflammatory Diseases, Hospital Clínic of Barcelona, Spain; 6Rheumatology Division, Universidade de São Paulo, Brazil; 7University of Bari; 8Rheumatology Unit, University and Azienda Ospedaliera Universitaria Integrata of Verona; 9University of Napoli "Federico II"; 10Università Vita-Salute San Raffaele, Milano; 11Luigi Sacco Hospital, University of Milano; 12Università di Pavia; 13University and AOU of Cagliari; 14AOU Policlinico Umberto I, Sapienza University of Rome; 15Unit of Rheumatology, ASL Sant' Andrea Hospital, Vercelli; 16University of Milano; 17Azienda Ospedaliero-Universitaria S. Anna, Ferrara; 18University of Trieste; 19University of Rome-Tor Vergata, Rome, Italy.
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CO:11:2 | Systemic lupus erythematosus with major neuropsychiatric involvement treated with anifrolumab: literature review and a case report Giulia Rizzo1, Fabio Congiu1, Elisabetta Chessa2, Marta Paola Pireddu1, Elena Ragusa1, Alessandra Oliva1, Marianna Salis1, Alberto Cauli1|2, Matteo Piga1|2 | 1SC Reumatologia, Dipartimento di Scienze Mediche e Salute Pubblica, Università di Cagliari Italy; 2SC Reumatologia, AOU Cagliari Italy
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PO:16:240 | Systemic Lupus Erythematosus Presenting as End-Stage Liver Disease: A Case Report and Literature Review Annamaria Tiso1, Stefania Caccavelli1, Giuseppina Caroppi1, Candida Tarullo1, Gaetano Serviddio1 | 1Policlinico Riuniti Foggia, Italy
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PO:14:205 | Primary antiphospholipid antibody syndrome: association between new classification criteria manifestations and a higher-risk disease phenotype Sara Ferrigno1, Vittorio Forte2, Marco Panetta1, Sergio Lisena1, Giorgia Ranucci2, Luigi De Marco1, Elisabetta Greco1, Alberto Bergamini1, Maria Sole Chimenti1, Paola Conigliaro1. | 1Rheumatology, allergology and clinical immunology, Department of Systems Medicine, University of Rome Tor Vergata, Rome, Italy; 2Hematology, Department of Biomedicine and Prevention, University of Rome Tor Vergata, Rome, Italy.
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PO:16:226 | Clinical Phenotypes of Systemic Lupus Erythematosus: An Exploratory Cluster Analysis in a Monocentric Cohort Richard Borrelli1, Stefania Nicola1, Federica Corradi1, Iuliana Badiu1, Luca Lo Sardo1, Marzia Boem1, Valentina Marmora1, Simone Negrini1, Luisa Brussino1 | 1SCDU Immunologia e Allergologia, AO Mauriziano, Dipartimento di Scienze Mediche, Università degli Studi di Torino, Italy
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CO:10:2 | Common variable immunodeficiency patients complicated by autoimmune and inflammatory rheumatic manifestations reveal high frequency of genetic variants potentially linked to inborn errors of immunity Paolo Semeraro1, Micol Frassi1, Silvia Clara Giliani2, Franco Franceschini1, Paolo Airò1. | 1Rheumatology and Clinical Immunology Unit, ERN ReCONNET, ASST Spedali Civili of Brescia and University of Brescia; 2Medical Genetic Laboratory, ASST Spedali Civili of Brescia and University of Brescia, Italy
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PO:14:195 | Real-world effectiveness of anifrolumab in achieving treatment targets and reducing systemic lupus erythematosus disease burden: 6-month interim analysis of the REVEAL study Chiara Cardelli1|2, Chiara Tani1, Luca Moroni3, Filippo Vesentini4, Francesca Bottazzi5, Micaela Fredi6, Ettore Silvagni7, Matteo Piga8, Flavia Riccio9, Fulvia Ceccarelli10, Ginevra De Marchi11, Edoardo Biancalana12, Gianluca Moroncini13, Rita Mulè14, Mariele Gatto15, Laura Coladonato16, Paola Conigliaro17, Maria Gerosa18, Andrea Picchianti Diamanti19, Benedetta Bianchi20, Federica Maiolini20, Michela Gasparotto20, Serena Guiducci20, Maria Ilenia De Andres20, Alberto Lo Gullo20, Silvia Noviello20, On Behalf Of The Reveal Investigators20, Marta Mosca1. | 1Rheumatology Unit, Department of Clinical and Experimental Medicine, University of Pisa, Pisa; 2Department of Medical Biotechnologies, University of Siena, Siena; 3Unit of Immunology, Rheumatology, Allergy and Rare Diseases, IRCCS San Raffaele Hospital, Milano; 4Rheumatology Unit, Department of Medicine, University of Padua, Padova; 5Department of Internal Medicine and Therapeutics, University of Pavia, Pavia; 6Rheumatology and Clinical Immunology, Department of Clinical and Experimental Sciences, University of Brescia, Brescia; 7Section of Rheumatology, Department of Medical Sciences, University of Ferrara; AOU Sant'Anna, Ferrara; 8Rheumatology Unit, Department of Medical Sciences and Public Health, University of Cagliari, Cagliari; 9Department of Precision Medicine, University of Campania Luigi Vanvitelli, Napoli; 10Rheumatology Unit, Dept. of Clinical Internal, Anesthesiological and Cardiovascular Sciences, Sapienza University of Rome, Roma; 11Division of Rheumatology, Department of Medicine, Azienda Sanitaria Universitaria del Friuli Centrale, Udine; 12Internal Interdisciplinary Medicine Unit, Department of Experimental and Clinical Medicine, University of Florence, Firenze; 13Department of Clinical and Molecular Sciences, Marche Polytechnic University, Ancona; 14Azienda Ospedaliero-Universitaria di Bologna, Internal Medicine and Rheumatology, IRCCS S. Orsola Malpighi, Bologna; 15Academic Rheumatology Centre, Department of Clinical and Biological Sciences, University of Turin; AO Mauriziano, Torino; 16Rheumatology Unit, Department of Precision and Regenerative Medicine and Ionian Area, University of Bari, Bari; 17Rheumatology, Allergology and Clinical Immunology, Department of Systems Medicine, Tor Vergata University of Rome, Roma; 18Clinical Rheumatology, ASST Gaetano Pini CTO; Department of Clinical Sciences and Community Health, University of Milano, Milano; 19Department of Clinical and Molecular Medicine, Sapienza University of Rome; AOU Sant'Andrea, Roma, Italy; 20Italian REVEAL Study Group Italy, Italy
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PO:16:233 | Efficacy of voclosporin on nephritis in patients with variable gain of function of TLR7 affected by lupus: clinical case Veronica Spedicato1, Laura Coladonato1, Marco Fornaro1, Marlea Lavista1, Daniele Sabella1, Marco Capodiferro1, Maria Morrone1, Crescenzio Scioscia1, Giuseppe Lopalco1, Florenzo Iannone1 | 1Unit of Rheumathology, Department of Precision and Regenerative Medicina, Area JonicaJ, University of Bari, Italy
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PO:17:253 | Unveiling the gap: a multicenter study on factors driving patient-physician discrepancies in assessing disease activity in systemic lupus erythematosus Giorgia Ingrid Gozzoli1, Micaela Fredi1, Federica Bonaso1, Silvia Ebe Lucia Della Pina1, Claudia Barison1, Irene Lorenzini4, Raffaele Pericotti4, Anna Mattiuzzo4, Marcelo Neto2, Sofia Azevedo3, Cláudia Oliveira3, Cesare Tomasi4, Luís Sousa Inês2, Franco Franceschini1. | 1Rheumatology and Clinical Immunology Unit, ASST Spedali Civili of Brescia, Brescia, Italy; 2Rheumatology Department, Centro Hospitalar Universitário de Coimbra - ULS Coimbra, Coimbra, Portugal; 3Rheumatology Department, ULS Aveiro, Aveiro, Portugal; 4Department of Clinical and Experimental Sciences, University of Brescia, Brescia, Italy.
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