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CO:06:3 | Clinical and laboratory markers for distinguishing VEXAS from Schnitzler's syndrome in male patients with skin involvement: insights from the International AIDA Network Registries Valeria Caggiano1, Jessica Sbalchiero1, Micol Frassi2, Andrea Hinojosa-Azaola3, Francesca Crisafulli2, Franco Franceschini2, Paolo Sfriso4, Sara Bindoli4, José Hernández-Rodríguez5, Henrique A. Mayrink Giardini6, Giuseppe Lopalco7, Florenzo Iannone7, Ombretta Viapiana8, Amato De Paulis9, Lorenzo Dagna10, Antonio Gidaro11, Serena Bugatti12, Matteo Piga13, Fabrizio Conti14, Rosetta Vitetta15, Cecilia Chighizola16, Marcello Govoni17, Giacomo Emmi18, Paola Triggianese19, Carmelo Gurnari19, Bruno Frediani1, Claudia Fabiani1, Luca Cantarini1, Antonio Vitale1, for the AIDA Network1 | 1Department of Medical Sciences, Surgery and Neurosciences, University of Siena; 2University of Brescia, Italy; 3Department of Immunology and Rheumatology, Mexico City, Mexico; 4Rheumatology Unit, University of Padova, Italy; 5Clinical Unit of Autoinflammatory Diseases, Hospital Clínic of Barcelona, Spain; 6Rheumatology Division, Universidade de São Paulo, Brazil; 7University of Bari; 8Rheumatology Unit, University and Azienda Ospedaliera Universitaria Integrata of Verona; 9University of Napoli "Federico II"; 10Università Vita-Salute San Raffaele, Milano; 11Luigi Sacco Hospital, University of Milano; 12Università di Pavia; 13University and AOU of Cagliari; 14AOU Policlinico Umberto I, Sapienza University of Rome; 15Unit of Rheumatology, ASL Sant' Andrea Hospital, Vercelli; 16University of Milano; 17Azienda Ospedaliero-Universitaria S. Anna, Ferrara; 18University of Trieste; 19University of Rome-Tor Vergata, Rome, Italy.
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PO:22:033 | Unraveling VEXAS syndrome: when skin manifestations and monoclonal gammopathy precede hematological myeloid alterations Laura Di Centa1, Simone Longhino1, Valeria Manfrè1, Stefania Sacco1, Luca Quartuccio1 | 1ASST Papa Giovanni XXIII, Bergamo, Italy
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PO:22:038 | Recurrent Pneumonias and Persistent Inflammation in VEXAS Syndrome: The Role of BAL in Differential Diagnosis Francesco Ghellere1, Bernardo D'Onofrio1, Maria Chiara Ditto1, Salvatore Panaro1, Francesca Piccione1|2, Giacomo Tanti1, Enrico Fusaro1, Simone Parisi1 | 1SC Reumatologia, Città della Salute e della Scienza Torino, Italy; 2Fondazione Ricerca Molinette Torino, Italy
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PO:10:141 | A Case Study: Navigating the VEXAS Syndrome Mimickers Erika Montabone1, Richard Borrelli1, Nicolò Rashidy1, Fabiana Giannoccaro2, Giuseppe Guida2, Federico Itri3, Renato Carignola4, Simone Negrini1, Stefania Nicola1, Luca Lo Sardo1, Iuliana Badiu1, Federica Corradi1, Ambra Bonvicino5, Maurizio Balbi6, Luisa Brussino1 | 1SCDU Immunologia e Allergologia, AO Mauriziano, Dipartimento di Scienze Mediche, Università degli Studi di Torino Torino, Italy; 2SSD Asma grave, malattie rare del polmone e fisiopatologia respiratoria, AOU San Luigi Gonzaga Orbassano, Italy; 3SCDU Medicina Interna ad indirizzo Ematologico, AOU San Luigi Gonzaga Orbassano, Italy; 4SCDU Medicina Interna, Scleroderma Unit, AOU San Luigi Gonzaga Orbassano, Italy; 5SCDU Dermatologia, Città della Salute e della Scienza di Torino Torino, Italy; 6SCDU Radiodiagnostica, AOU San Luigi Gonzaga, Dipartimento di Oncologia Orbassano, Italy
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PO:21:028 | A difficult case of VEXAS syndrome: management of myelodysplastic syndrome associated with systemic inflammation and infectious complications Sandra Lombardi1, Monica Regis1, Stefano De Luca1, Monica Poiani2, Rossella Stella2, Elisa Lucchini2, Francesco Zaja2, Fabio Fiammengo1 | 1SC Medicina Interna, Azienda Sanitaria Universitaria Giuliano Isontina, Gorizia; 2SC Ematologia, Azienda Sanitaria Universitaria Giuliano Isontina, Trieste, Italy
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