Case Reports Open access

Rare in the rare: Kikuchi-Fujimoto disease associated with connective tissue disorders. A report of our experience

Authors

Published
4 August 2025
Section
Case Reports
DOI
10.4081/reumatismo.2025.1853

Abstract

Kikuchi-Fujimoto disease (KFD) is a rare and benign lymphadenopathy of unknown etiology. Usually, it is an isolated and self-limiting condition requiring no specific therapy; however, in some cases, it may be associated with an autoimmune disease. Here, we report three cases of KFD developing an associated autoimmune connective disorder: the first case presented with Sjögren’s syndrome, and the other two had a diagnosis of systemic lupus erythematosus.

Keywords

References

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