Case Reports
4 August 2025
Early Access
Rare in the rare: Kikuchi-Fujimoto disease associated with connective tissue disorders. A report of our experience
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All claims expressed in this article are solely those of the authors and do not necessarily represent those of their affiliated organizations, or those of the publisher, the editors and the reviewers. Any product that may be evaluated in this article or claim that may be made by its manufacturer is not guaranteed or endorsed by the publisher.
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Kikuchi-Fujimoto disease (KFD) is a rare and benign lymphadenopathy of unknown etiology. Usually, it is an isolated and self-limiting condition requiring no specific therapy; however, in some cases, it may be associated with an autoimmune disease. Here, we report three cases of KFD developing an associated autoimmune connective disorder: the first case presented with Sjögren's syndrome, and the other two had a diagnosis of systemic lupus erythematosus.
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How to Cite
Rare in the rare: Kikuchi-Fujimoto disease associated with connective tissue disorders. A report of our experience. (2025). Reumatismo. https://doi.org/10.4081/reumatismo.2025.1853
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